@prefix    owl: <http://www.w3.org/2002/07/owl#> .
@prefix   rdfs: <http://www.w3.org/2000/01/rdf-schema#> .
@prefix    rdf: <http://www.w3.org/1999/02/22-rdf-syntax-ns#> .
@prefix biopax: <http://www.reactome.org/biopax/48887#> .
@prefix    obo: <http://purl.obolibrary.org/obo/> .

# Named toplevel resources (13)

<http://example.org>
	a owl:Ontology ;
	owl:imports <http://purl.obolibrary.org/obo/go.owl> ,
		    <http://purl.obolibrary.org/obo/go/extensions/lego-relations.owl> .

obo:UniProtKB_P35475
	rdfs:label "IDUA"@em ,
		   "UniProt:P35475 IDUA"@em .

obo:UniProtKB_Q12794
	rdfs:label "HYAL1"@em ,
		   "LUCA1"@em ,
		   "UniProt:Q12794 HYAL1"@em .

biopax:BiochemicalReaction3124
	a obo:GO_0003674 ;
	obo:BFO_0000050 biopax:Pathway742 ;
	obo:directly_activates biopax:BiochemicalReaction3125 ,
			       biopax:BiochemicalReaction3126 ,
			       biopax:Catalysis1352 ,
			       biopax:Catalysis1353 ;
	rdfs:label "DSPG and CSPG translocate to the lysosome for degradation"@em .

biopax:BiochemicalReaction3125
	a [ a owl:Restriction ;
	    owl:onProperty obo:BFO_0000066 ;
	    owl:someValuesFrom obo:GO_0043202
	  ] ,
	  obo:GO_0016798 ;
	obo:BFO_0000050 biopax:Pathway742 ;
	obo:directly_activates biopax:BiochemicalReaction3127 ,
			       biopax:Catalysis1354 ;
	rdfs:label "DS is cleaved from its proteoglycan"@em .

biopax:BiochemicalReaction3126
	a [ a owl:Restriction ;
	    owl:onProperty obo:BFO_0000066 ;
	    owl:someValuesFrom obo:GO_0043202
	  ] ,
	  obo:GO_0016798 ;
	obo:BFO_0000050 biopax:Pathway742 ;
	obo:directly_activates biopax:BiochemicalReaction3131 ,
			       biopax:Catalysis1358 ;
	rdfs:label "CS is cleaved from its proteoglycan"@em .

biopax:BiochemicalReaction3127
	a [ a owl:Restriction ;
	    owl:onProperty obo:BFO_0000066 ;
	    owl:someValuesFrom obo:GO_0043202
	  ] ,
	  obo:GO_0003943 ;
	obo:BFO_0000050 biopax:Pathway742 ;
	obo:directly_activates biopax:BiochemicalReaction3128 ,
			       biopax:BiochemicalReaction3132 ,
			       biopax:Catalysis1355 ,
			       biopax:Catalysis1359 ;
	rdfs:label "Arylsulfatase B (ARSB) hydrolyses sulfate groups from GalNAc 4-sulfate units of DS"@em .

biopax:BiochemicalReaction3128
	a [ a owl:Restriction ;
	    owl:onProperty obo:BFO_0000066 ;
	    owl:someValuesFrom obo:GO_0043202
	  ] ,
	  obo:GO_0004423 ;
	obo:BFO_0000050 biopax:Pathway742 ;
	obo:directly_activates biopax:BiochemicalReaction3129 ,
			       biopax:Catalysis1356 ;
	rdfs:label "Iduronate 2-sulfatase (IDS) hydrolyses sulfates from L-iduronate 2-sulfate units of dermatan sulfate"@em .

biopax:BiochemicalReaction3129
	a [ a owl:Restriction ;
	    owl:onProperty obo:BFO_0000066 ;
	    owl:someValuesFrom obo:GO_0043202
	  ] ,
	  obo:GO_0004563 ;
	obo:BFO_0000050 biopax:Pathway742 ;
	obo:directly_activates biopax:BiochemicalReaction3130 ,
			       biopax:Catalysis1357 ;
	rdfs:label "Beta-hexosaminidase A (BHEXA) cleaves the terminal GalNAc from DS"@em .

biopax:BiochemicalReaction3130
	a [ a owl:Restriction ;
	    owl:onProperty obo:BFO_0000066 ;
	    owl:someValuesFrom obo:GO_0043202
	  ] ,
	  [ a owl:Restriction ;
	    owl:onProperty obo:enabled_by ;
	    owl:someValuesFrom obo:UniProtKB_P35475
	  ] ,
	  obo:GO_0003940 ;
	obo:BFO_0000050 biopax:Pathway742 ;
	rdfs:label "Alpha-L-iduronidase (IDUA) hydrolyses the unsulfated alpha-L-iduronosidic linkage in DS"@em .

biopax:BiochemicalReaction3131
	a [ a owl:Restriction ;
	    owl:onProperty obo:BFO_0000066 ;
	    owl:someValuesFrom obo:GO_0043202
	  ] ,
	  obo:GO_0003943 ;
	obo:BFO_0000050 biopax:Pathway742 ;
	obo:directly_activates biopax:BiochemicalReaction3132 ,
			       biopax:Catalysis1359 ;
	rdfs:label "Arylsulfatase B (ARSB) hydrolyses sulfate groups from GalNAc 4-sulfate units of CS"@em .

biopax:BiochemicalReaction3132
	a [ a owl:Restriction ;
	    owl:onProperty obo:enabled_by ;
	    owl:someValuesFrom obo:UniProtKB_Q12794
	  ] ,
	  [ a owl:Restriction ;
	    owl:onProperty obo:BFO_0000066 ;
	    owl:someValuesFrom obo:GO_0043202
	  ] ,
	  obo:GO_0004415 ;
	obo:BFO_0000050 biopax:Pathway742 ;
	rdfs:label "Hyaluronidase 1 (HYAL1) hydrolyses 1-4 linkages between GalNAc and D-glucuronate residues in CS."@em .

biopax:Pathway742
	a obo:GO_0008150 ;
	rdfs:label "CS/DS degradation"@em .